血管炎胸部表现学习PPT教案.pptx
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血管炎胸部表现学习PPT教案.pptx

血管炎胸部表现学习PPT教案.pptx

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血管炎的病理基础是大小不等的动脉、静脉、微血管管壁及其周围的炎性改变,最终导致血管管腔变窄、循环受阻、受累器官出现功能障碍;该疾病临床表现多样、预后与受累器官及炎症严重程度有关。原发性&继发性分类:大血管炎-大动脉炎、巨细胞动脉炎;中血管炎-结节性多动脉炎,川琦病;小血管炎-韦格纳肉芽肿、显微镜下多血管炎、Churg-strauss综合征、过敏性紫癜;大动脉炎TakayasuArteritis巨细胞动脉炎GiantCellArteritis韦格纳肉芽肿WegenerGranulomatosis变应性肉芽肿性血管炎Churg-StraussSyndrome显微镜下多血管炎MicroscopicPolyangiitis白塞病BehçetDiseaseBehçetdiseaseina26-year-oldwomanwhopresentedwithdyspneaTheprimaryvasculitidesareraredisorders.Theirsignsandsymptomsarenonspecificandoverlapwiththoseofinfections,connectivetissuediseases,andmalignancies.Anintegratedclinical,radiologic,andsometimeshistologicapproachisneeded.WhentheclinicalpresentationisanabnormallungCTorchestradiographicfinding,shortnessofbreath,orrenalfailure,symptomssuchasuveitis,unusualrashes,arthritis,or“sinustroubles”mustberememberedandconsidered.Takayasuarteritis&GCABehçetdiseaseisthemostcommoncauseofpulmonaryarteryaneurysms.Thepresenceofotherwiseunexplainednodularorcavitarydiseaseshouldraisethesuspicionofvasculitis(WegenerGranulomatosis).CSSshouldbesuspectedwhenpatchyground-glassopacitiesorconsolidationsareseeninapatientwithahistoryofasthmawhoalsopresentswitheosinophilia.谢谢!Behçetdiseaseina26-year-oldwomanwhopresentedwithdyspnea