溶血性贫血.ppt
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溶血性贫血.ppt

溶血性贫血.ppt

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HemolyticAnemiaContentsOverviewofAnemiaDefinition:Hemolysis&HemolyticAnemiaPathophysiologyDiagnosticTestingDiagnosticTesting(continued)DiagnosticTesting(continued)溶血性黄疸发生机理示意图AlgorithmfortheevaluationofhemolyticanemiaEtiologyofHemolysisImmuneHemolyticAnemia:classificationImmuneHemolyticAnemia:GeneralPrinciplesImmuneHemolyticAnemia:GeneralPrinciplesImmuneHemolyticAnemia:GeneralPrinciplesIgGandC3bmediatedhemolysisAutoimmunehemolyticanemia:WarmAIHASpherocytes(arrows),characterizedbyalackofcentralpallor,occurinbothautoimmunehemolyticanemiaandhereditaryspherocytosis.Autoimmunehemolyticanemia:coldAIHAAutoimmunehemolyticanemia:TreatmentAutoimmunehemolyticanemia:Treatment(continued)Drug-inducedhemolysisDrug-Induced(examples)AlloimmuneHemolysis:HemolyticTransfusionReactionDonorBloodIncompatibilitieswithintheRhbloodgroupsystemMicroangiopathichemolyticanemia(MAHA)injuredvascularendotheliumMicroangiopathichemolyticanemia(continued)InfectionPeripheralSmearofMalariaParoxysmalnocturnalhemoglobinuria(PNH)Paroxysmalnocturnalhemoglobinuria(PNH)(continued)Paroxysmalnocturnalhemoglobinuria(PNH)(continued)InheritedDisordersEnzymopathies:G6PDdeficiencyFunctionofG6PDG6PDDeficiency(continued)PeripheralSmearw/HeinzBodiesAgentsthatPrecipitateHemolysisinPatientswithG6PDDeficiencyMembranopathies:HereditarySpherocytosisHereditarySpherocytosis54NormalredbloodcellsunderEMSHemoglobinopathies:ThalassemiasBloodfilmofthalassemiasα-ThalassemiaHemoglobinopathies:SicklecellanemiaPeripheralSmearofSickleCellSummaryThankyou!